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Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl

Received: 5 July 2022     Accepted: 20 July 2022     Published: 28 July 2022
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Abstract

Choledocal cyst (CC) is a rare congenital cystic dilation of bile duct and can be associated with serious complications including malignancy and inflammation of the surrounding anatomy. Approximately 80% of CC is diagnosed in infants and young children in their first decade of life. Complete surgical resection is recommended in patients with choledochal malformations with excellent outcome. Hereby we aimed to describe diagnosis and management aspects of choledochal cyst. A two years old girl complained intermittent abdominal pain in her upper right quadrant abdomen, accompanied with fever, nausea and vomiting and decrease of appetite. Physical examination, we found jaundice on sclera and palpabled liver 2 fingers below the costal arch. Abdominal ultrasound revealed cystic mass in right lower lobe, suggestive of hepatic cyst with inflammation of cystic head of pancreas and minimal free fluid in lumen. Abdominal CT-scan without contrast showed a choledocal cyst classified as Todani Type IV. A cyst in the bile duct was found during surgical procedure. In conclusion choledocal cyst as one of the differential diagnoses in children, which is characterized by intermittent right upper abdominal pain, jaundice and fever. Appropriate surgical measures should be undertaken to avoid complications.

Published in American Journal of Pediatrics (Volume 8, Issue 3)
DOI 10.11648/j.ajp.20220803.13
Page(s) 168-172
Creative Commons

This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.

Copyright

Copyright © The Author(s), 2022. Published by Science Publishing Group

Keywords

Children, Choledocal Cysts, Extrahepatal Cholestasis

References
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[12] De Angelis P, Foschia F, Romeo E, Caldaro T, Rea F, di Abriola GF, et al. Role of Endoscopic Retrograde Cholangiopancreatography in Diagnosis and Management of Congenital Choledochal Cysts: 28 Pediatric Cases. J Pediatr Surg. 2012; 47 (5): 885-8. doi: 10.1016/j.jpedsurg.2012.01.040.
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Cite This Article
  • APA Style

    Luh Made Diah Wulandari Artana, I Gusti Ngurah Sanjaya Putra, Kadek Deddy Ariyanta, I Putu Gede Karyana, Ni Nyoman Metriani Nesa, et al. (2022). Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl. American Journal of Pediatrics, 8(3), 168-172. https://doi.org/10.11648/j.ajp.20220803.13

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    ACS Style

    Luh Made Diah Wulandari Artana; I Gusti Ngurah Sanjaya Putra; Kadek Deddy Ariyanta; I Putu Gede Karyana; Ni Nyoman Metriani Nesa, et al. Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl. Am. J. Pediatr. 2022, 8(3), 168-172. doi: 10.11648/j.ajp.20220803.13

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    AMA Style

    Luh Made Diah Wulandari Artana, I Gusti Ngurah Sanjaya Putra, Kadek Deddy Ariyanta, I Putu Gede Karyana, Ni Nyoman Metriani Nesa, et al. Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl. Am J Pediatr. 2022;8(3):168-172. doi: 10.11648/j.ajp.20220803.13

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  • @article{10.11648/j.ajp.20220803.13,
      author = {Luh Made Diah Wulandari Artana and I Gusti Ngurah Sanjaya Putra and Kadek Deddy Ariyanta and I Putu Gede Karyana and Ni Nyoman Metriani Nesa and I Made Darmajaya},
      title = {Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl},
      journal = {American Journal of Pediatrics},
      volume = {8},
      number = {3},
      pages = {168-172},
      doi = {10.11648/j.ajp.20220803.13},
      url = {https://doi.org/10.11648/j.ajp.20220803.13},
      eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajp.20220803.13},
      abstract = {Choledocal cyst (CC) is a rare congenital cystic dilation of bile duct and can be associated with serious complications including malignancy and inflammation of the surrounding anatomy. Approximately 80% of CC is diagnosed in infants and young children in their first decade of life. Complete surgical resection is recommended in patients with choledochal malformations with excellent outcome. Hereby we aimed to describe diagnosis and management aspects of choledochal cyst. A two years old girl complained intermittent abdominal pain in her upper right quadrant abdomen, accompanied with fever, nausea and vomiting and decrease of appetite. Physical examination, we found jaundice on sclera and palpabled liver 2 fingers below the costal arch. Abdominal ultrasound revealed cystic mass in right lower lobe, suggestive of hepatic cyst with inflammation of cystic head of pancreas and minimal free fluid in lumen. Abdominal CT-scan without contrast showed a choledocal cyst classified as Todani Type IV. A cyst in the bile duct was found during surgical procedure. In conclusion choledocal cyst as one of the differential diagnoses in children, which is characterized by intermittent right upper abdominal pain, jaundice and fever. Appropriate surgical measures should be undertaken to avoid complications.},
     year = {2022}
    }
    

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  • TY  - JOUR
    T1  - Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl
    AU  - Luh Made Diah Wulandari Artana
    AU  - I Gusti Ngurah Sanjaya Putra
    AU  - Kadek Deddy Ariyanta
    AU  - I Putu Gede Karyana
    AU  - Ni Nyoman Metriani Nesa
    AU  - I Made Darmajaya
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    DO  - 10.11648/j.ajp.20220803.13
    T2  - American Journal of Pediatrics
    JF  - American Journal of Pediatrics
    JO  - American Journal of Pediatrics
    SP  - 168
    EP  - 172
    PB  - Science Publishing Group
    SN  - 2472-0909
    UR  - https://doi.org/10.11648/j.ajp.20220803.13
    AB  - Choledocal cyst (CC) is a rare congenital cystic dilation of bile duct and can be associated with serious complications including malignancy and inflammation of the surrounding anatomy. Approximately 80% of CC is diagnosed in infants and young children in their first decade of life. Complete surgical resection is recommended in patients with choledochal malformations with excellent outcome. Hereby we aimed to describe diagnosis and management aspects of choledochal cyst. A two years old girl complained intermittent abdominal pain in her upper right quadrant abdomen, accompanied with fever, nausea and vomiting and decrease of appetite. Physical examination, we found jaundice on sclera and palpabled liver 2 fingers below the costal arch. Abdominal ultrasound revealed cystic mass in right lower lobe, suggestive of hepatic cyst with inflammation of cystic head of pancreas and minimal free fluid in lumen. Abdominal CT-scan without contrast showed a choledocal cyst classified as Todani Type IV. A cyst in the bile duct was found during surgical procedure. In conclusion choledocal cyst as one of the differential diagnoses in children, which is characterized by intermittent right upper abdominal pain, jaundice and fever. Appropriate surgical measures should be undertaken to avoid complications.
    VL  - 8
    IS  - 3
    ER  - 

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Author Information
  • Department of Child Health, Sanglah Hospital, Faculty of Medicine, Udayana University, Denpasar, Indonesia

  • Department of Child Health, Sanglah Hospital, Faculty of Medicine, Udayana University, Denpasar, Indonesia

  • Department of Surgery, Sanglah Hospital, Faculty of Medicine, Udayana University, Denpasar, Indonesia

  • Department of Child Health, Sanglah Hospital, Faculty of Medicine, Udayana University, Denpasar, Indonesia

  • Department of Child Health, Sanglah Hospital, Faculty of Medicine, Udayana University, Denpasar, Indonesia

  • Department of Surgery, Sanglah Hospital, Faculty of Medicine, Udayana University, Denpasar, Indonesia

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